苯丙酮尿症患儿血苯丙氨酸浓度宜维持在
A、0.06~0.12mmol/L(1~2m/L)
B、0.06~0.24mmol/L(1~4mg/L)
C、0.12~0.24mmol/L(2~4mg/L)
D、0.12~0.48mmol/L(2~8mg/L)
E、0.12~0.6mmol/L(2~10mg/L)
第1题:
苯丙酮尿症患儿血苯丙氨酸浓度宜维持在
A.0.06~0.12mmol/L(1~2mg/L)
B.0.06~0.24mmol/L(1~4mg/L)
C.0.12~0.24mmol/L(2~4mg/L)
D.0.12~0.48mmol/L(2~8mg/L)
E.0.12~0.6mmol/L(2~10mg/L)
第2题:
苯丙酮尿症患儿血苯丙氨酸浓度宜维持在
A、0.06~0.12mmol(1~2mg/dl)
B、0.06~0.24mmol(1~4mg/dl)
C、0.12~0.24mmol/L(2~4mg/dl)
D、0.12~0.48mmol/L(2~8mg/dl)
E、0.12~0.6mmol/L(2~10mg/dl)
第3题:
第4题:
苯丙酮尿症( )
A.染色体核型为:46,XX(或XY)/47,+21
B.血苯丙氨酸浓度>0.24mmol/L(4mg/dl)
C.染色体核型为:45,XO/46,XX
D.染色体核型为:48,XXXY
E.血清铜蓝蛋白值:50mg/L
第5题: